Youth with sickle cell disease (SCD) experience a number of symptoms that may interfere with daily functioning and quality of life. Some researchers and clinicians argue that treatment efforts should target functioning and living in line with self-identified values rather than symptom reduction. In research with adults with chronic pain, results indicate that improvement in functioning predicts success in living in line with values. The purpose of this study was to examine the relation between functional disability and values-based living in children with SCD. A secondary aim was to examine whether the relation between functioning and valued living differed by sex of the patient. Participants included twenty-eight 8- to 18-year-olds diagnosed with SCD. Youth completed measures of pain, functioning, and success in valued living. After controlling for pain, healthy functioning predicted success in valued living, however this relation was found in boys and not girls. Implications are discussed.
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