Laparoscopic Hemihysterectomy in a Case of Uterus Didelphys with Nonfused Rudimentary Uterine Horns with Functioning Endometria and Complete Cervical-Vaginal Agenesis

Abnormalities of the Müllerian system exist in a variety of forms. Conventional anomalies are easy to manage, but a rare combination of anomalies requires good clinical judgment to diagnose and manage. In this paper, we report on a 17-year-old girl with two rudimentary horns, with functional endometrium in one horn, and cervicovaginal agenesis. She was diagnosed to have vaginal agenesis 2 years prior and underwent vaginoplasty. The presence of an obstructive uterine anomaly was overlooked. She presented to us with cyclic abdominal pain 2 years later. On evaluation, a functional rudimentary horn was diagnosed and removed laparoscopically. Abnormalities in vertical fusion may rarely coexist with defects in lateral fusion and must be looked for in any adolescent with cyclical abdominal pain.