Divergent Ependymal Tumor (Ependymoblastoma/Anaplastic Ependymoma) of the Posterior Fossa: An Uncommon Case Observed in a Child

Abstract

We report a divergent ependymal tumor of the posterior fossa (ependymoblastoma/anaplastic ependymoma) observed in an 8-year-old boy. The tumor showed the histological pattern typical of an ependymoblastoma (tubular-papillary fetaloid architecture with stratification of the tumor cells) next to areas in which findings typical of an anaplastic ependymoma were detected. The immunohistochemical study confirmed our diagnostic suspicion, allowing us to establish a differential diagnosis with other entities such as medulloblastoma, medulloepithelioma, atypical rhabdoid/teratoid tumor, or metastases.

Keywords

ependymoblastoma anaplastic ependymoma divergent ependymal tumor

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