The nephrotic syndrome (NS) is reportedly as sociated with an increased risk of thromboembolic dis ease. We describe the case of an 8-year-old child with a steroid-responsive NS who developed a longitudinal si nus venous thrombosis. No family thrombophilic ten dency was found. To our knowledge, this is the second case published with these clinical characteristics. We sug gest that the sinus venous thrombosis was precipitated by the low levels of antithrombin III and hypoalbuminemia. Moreover, steroids probably played an etiological role. Key Words: Nephrotic syndrome—Sinus venous throm bosis—Venous thrombosis—Antithrombin III.
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