Sjögren Reticular Dystrophy of the Retinal Pigment Epithelium: A Case Report

Abstract

Purpose

To describe the clinical manifestations in a patient with Sjögren reticular dystrophy of the retinal pigment epithelium, and the evolution of the disease over a 20-year follow-up period.

Case Report

A 45-year-old woman with Sjögren reticular dystrophy of the retinal pigment epithelium was seen for the first time in 1983; the patient underwent 20 years of annual check-ups.

Results

Over the follow-up period, fundus photographs, computerized perimetry, electroretinogram, and electro-oculogram findings had either normal or slightly subnormal outcome.

Conclusions

The results confirm that this disease involves only the retinal pigment epithelium and should not be considered a central tapeto-retinal degeneration or late onset retinopathy.

Keywords

Reticular dystrophy of retinal pigment epithelium Sjögren reticular dystrophy Pattern dystrophy of the retinal pigment epithelium

Get full access to this article

View all access options for this article.

References

Sjögren

. Distrophia reticularis laminae pigmentosae retinae. Acta Ophthalmol 1950; 28: 279–95.

Kingham

J.D.

Fenzl

R.E.

Willerson

Aaberg

T.M.

. Reticular dystrophy of the retinal pigment epithelium. A clinical and electrophysiologic study of three generations. Arch Ophthalmol 1978; 96: 1177–84.

Blodi

F.C.

. The pathology of central TRD (hereditary macular degeneration). Trans Am Acad Ophthalmol Otolaryngol 1966; 70: 1047–53.

Waardenburg

P.J.

. Genetics and Ophthalmology, vol. 2. Assen, Netherlands: Royal van Gorcum; 1963: 1685–6.

Hsieh

R.C.

Fine

B.S.

Lyons

J.S.

. Patterned dystrophies of the retinal pigment epithelium. Arch Ophthalmol 1977; 95: 429–35.

Deutman

A.F.

Rumke

A.M.L.

. Reticular dystrophy of retinal pigment epithelium. Arch Ophthalmol 1969; 82: 4–9.

Alezzandrini

A.A.

. La retino-Fluoresceinografia en las alteraciones del epitelio pigmentario de la retina. Arch Ophthalmol 1971; 46: 13–20.

Fishman

G.A.

Woolf

M.B.

Goldberg

M.F.

Busse

. Reticular tapeto-retinal dystrophy as a possible late stage of Sjögren's reticular dystrophy. Br J Ophthalmol 1976; 60: 35–40.

Donnel

F.E.

Schatz

Reid

Green

W.R.

. Autosomal dominant dystrophy of the retinal pigment epithelium. Arch Ophthalmol 1979; 97: 680–3.

10.

Girard

Setbon

Forest

Coscas

. Dystrophies en réreau de l'epithélium pigmentaire (dystrophies macroreticulaires et en aile de papillon). J Fr Ophtalmol 1980; 3: 101–6.

11.

Marmor

M.F.

Byers

. Pattern dystrophy of the retinal pigment epithelium. Am J Ophthalmol 1977; 84: 32–44.

12.

Cortin

Archer

Maumenee

J.H.

Fejock

Speros

. A patterned macular dystrophy with yellow plaques and atrophic changes. Br J Ophthalmol 1980; 64: 127–34.

13.

Marano

Deutman

A.F.

Pinckers

A.J.

Aandekerk

A.L.

Rjjneveld

W.J.

. Reticular dystrophy of the retinal pigment epithelium and choroidal neovascularization. A fluorescein and ICGV study. Acta Ophthalmol 1997; 75: 22–7.