Nevoid Basal Cell Carcinoma Syndrome Presenting as Chronic Maxillary Sinusitis

Nevoid basal cell carcinoma syndrome is a very rare condition consisting of nevoid basal cell epitheliomas, jaw cysts, and skeletal abnormalities. This article describes the first reported presentation of this syndrome as maxillary sinusitis. The multiple and varied features of this rare syndrome are discussed together with management and treatment modalities.